Alveolar rhabdomyosarcoma in an adolescent male patient - case report and current perspectives Vol. We present the case of an adolescent male patient treated in our Department for a tumoral mass located in the middle third of the forearm.
Magnetic resonance imaging MRI and angiography-computed tomography angio-CT showed a large mass located in the muscles of the anterior compartment of the forearm. Surgical treatment consisted of tumor ablation including sarcoma cancer pediatric resection of the radial and ulnar arteries and of the median nerve, followed by saphenous autograft vascular bypass.
The treatment plan was based on tumor type, histological grading highage, tumor size greater than 5 cm, unfavorable location, postoperative tumor, node, metastasis TNM stage II, presence of microscopic tumoral tissue in the margins of the resected piece, lymph node metastases N1 and bone metastases M1 found on positron-emission tomography PET -CT according to the German soft tissue sarcoma study CWS -IV protocol.
The chemotherapy used Carboplatin and Topotecan. Survival was less than two years after the initial presentation.
Adolescent extremity masses should raise suspicion to exclude serious malignancy. Despite early diagnosis and use of multimodal therapies, alveolar RMS prognostic remains unpredictable.